Date amended:
External
Statements of Principles
Current RMA Instruments:
Reasonable Hypothesis SOP
61 of 2016
Balance of Probabilities SOP
62 of 2016
Changes from previous Instruments:

ICD Coding:
  • ICD-9-CM Codes: 387
  • ICD-10-AM Codes: H80
Brief description

Otosclerosis is a metabolic bone disease in which scarred bone is formed in the middle ear, resulting in conductive hearing loss.

Confirming the diagnosis

Diagnosis is based on characteristic clinical findings, which include progressive conductive hearing loss, a normal tympanic membrane, and no evidence of middle ear inflammation.

The relevant medical specialist is an ENT surgeon.

Additional diagnoses covered by SOP
  • Cochlear otosclerosis
  • Otospongiosis
Clinical onset

Clinical onset will usually be when hearing loss, subsequently confirmed to be due to otosclerosis, is first recorded. Onset is typically between ages 10 and 30.

Clinical worsening

The only SOP worsening factor is for inablitiy to obtain appropriate clinical management. Treament may involve observation, dietary supplements (sodium fluoride), surgery or hearing aids.  Progression of the disease and the conductive hearing loss may be slowed by diet therapy.