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Creutzfeldt-Jakob Disease F005
In this section
Current RMA Instruments
|Reasonable Hypothesis SOP||80 of 2022|
|Balance of Probabilities SOP||81 of 2022|
Changes from previous Instruments
- ICD-10-AM Code: A81.0
This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease. CJD is a very rare disease. No case of variant CJD has ever been reported in Australia (as at Sep ‘22).
Confirming the diagnosis
This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.
Additional diagnoses covered by SOP
- Classical Creutzfeldt Jakob disease
- Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
- Kuru - non-SOP
- Other forms of dementia
Mean age of onset is around 60. The typical clinical presentation is with rapid neuropsychiatric decline.
There are no clinical worsening factors in the SOP.