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Creutzfeldt-Jakob Disease F005

Last amended 
29 June 2015
Current RMA Instruments:
Reasonable Hypothesis SOP
76 of 2014
Balance of Probabilities SOP
77 of 2014
Changes from Previous Instruments:

SOP Bulletin 177

ICD Coding:
  • ICD-9-CM Codes: 046.1
  • ICD-10-AM Codes: A81.0

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (at Sep ‘14).

Is specific diagnostic evidence required to apply the SOP? – Yes.

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Are there sub-factors that require specific information? – Yes.

There are factors covering variant CJD only.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru, ICD code 046.0
Unconfirmed diagnosis

If, after applying the above information, you are unable to confirm the diagnosis, you should then seek medical officer advice about further investigation.