Creutzfeldt-Jakob Disease F005

Current RMA Instruments
Reasonable Hypothesis SOP
80 of 2022
Balance of Probabilities SOP
81 of 2022
Changes from previous Instruments

ICD Coding
  • ICD-10-AM Code: A81.0
Brief description

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (as at Sep ‘22).

Confirming the diagnosis

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru - non-SOP
  • Other forms of dementia
Clinical onset

Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.

Clinical worsening

There are no clinical worsening factors in the SOP.

Source URL: https://clik.dva.gov.au/ccps-medical-research-library/sops-grouped-icd-body-system/c-d/creutzfeldt-jakob-disease-f005-a810

Last amended

Rulebase for Creutzfeldt-Jakob disease

<h5><strong>Current RMA Instruments</strong></h5><table border="1" cellpadding="1" cellspacing="1"><tbody><tr><td><address><a href="http://www.rma.gov.au/assets/SOP/2022/4ad3e46aa2/080.pdf&quot; target="_blank">Reasonable Hypothesis SOP</a></address></td><td>80 of 2022</td></tr><tr><td><address><a href="http://www.rma.gov.au/assets/SOP/2022/d8a7dfe380/081.pdf&quot; target="_blank">Balance of Probabilities SOP </a></address></td><td>81 of 2022</td></tr></tbody></table><h5>Changes from previous Instruments</h5><p><drupal-media data-entity-type="media" data-entity-uuid="721b9342-2587-4df4-a3d0-e50bee5a0d67" data-view-mode="wysiwyg"></drupal-media></p><h5>ICD Coding</h5><ul><li>ICD-10-AM Code: A81.0</li></ul><h5>Brief description</h5><p>This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (as at Sep ‘22).</p><h5>Confirming the diagnosis</h5><p>This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.</p><h5>Additional diagnoses covered by SOP</h5><ul><li>Classical Creutzfeldt Jakob disease</li><li>Variant Creutzfeldt Jakob disease</li></ul><h5>Conditions excluded from SOP</h5><ul><li>Kuru - non-SOP</li><li>Other forms of dementia</li></ul><h5>Clinical onset</h5><p>Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.</p><h5>Clinical worsening</h5><p>There are no clinical worsening factors in the SOP.</p>

Source URL: https://clik.dva.gov.au/ccps-medical-research-library/statements-principles/c-d/creutzfeldt-jakob-disease-f005-a810/rulebase-creutzfeldt-jakob-disease

Dura mater graft

Current RMA Instruments
Reasonable Hypothesis SOP
80 of 2022
Balance of Probabilities SOP
81 of 2022
Changes from previous Instruments

ICD Coding
  • ICD-10-AM Code: A81.0
Brief description

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (as at Sep ‘22).

Confirming the diagnosis

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru - non-SOP
  • Other forms of dementia
Clinical onset

Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.

Clinical worsening

There are no clinical worsening factors in the SOP.

Source URL: https://clik.dva.gov.au/ccps-medical-research-library/statements-principles/c-d/creutzfeldt-jakob-disease-f005-a810/rulebase-creutzfeldt-jakob-disease/dura-mater-graft

Surgery to the central nervous system or cornea

Current RMA Instruments
Reasonable Hypothesis SOP
80 of 2022
Balance of Probabilities SOP
81 of 2022
Changes from previous Instruments

ICD Coding
  • ICD-10-AM Code: A81.0
Brief description

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (as at Sep ‘22).

Confirming the diagnosis

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru - non-SOP
  • Other forms of dementia
Clinical onset

Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.

Clinical worsening

There are no clinical worsening factors in the SOP.

Source URL: https://clik.dva.gov.au/ccps-medical-research-library/statements-principles/c-d/creutzfeldt-jakob-disease-f005-a810/rulebase-creutzfeldt-jakob-disease/surgery-central-nervous-system-or-cornea

Treatment with human pituitary gonadotrophins

Current RMA Instruments
Reasonable Hypothesis SOP
80 of 2022
Balance of Probabilities SOP
81 of 2022
Changes from previous Instruments

ICD Coding
  • ICD-10-AM Code: A81.0
Brief description

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (as at Sep ‘22).

Confirming the diagnosis

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru - non-SOP
  • Other forms of dementia
Clinical onset

Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.

Clinical worsening

There are no clinical worsening factors in the SOP.

Source URL: https://clik.dva.gov.au/ccps-medical-research-library/statements-principles/c-d/creutzfeldt-jakob-disease-f005-a810/rulebase-creutzfeldt-jakob-disease/treatment-human-pituitary-gonadotrophins

Treatment with human pituitary growth hormone

Current RMA Instruments
Reasonable Hypothesis SOP
80 of 2022
Balance of Probabilities SOP
81 of 2022
Changes from previous Instruments

ICD Coding
  • ICD-10-AM Code: A81.0
Brief description

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (as at Sep ‘22).

Confirming the diagnosis

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru - non-SOP
  • Other forms of dementia
Clinical onset

Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.

Clinical worsening

There are no clinical worsening factors in the SOP.

Source URL: https://clik.dva.gov.au/ccps-medical-research-library/statements-principles/c-d/creutzfeldt-jakob-disease-f005-a810/rulebase-creutzfeldt-jakob-disease/treatment-human-pituitary-growth-hormone