You are here
Fibromuscular Dysplasia G030
Current RMA Instruments
|Reasonable Hypothesis SOP||79 of 2016|
|Balance of Probabilities SOP||80 of 2016|
Changes from previous Instruments
- ICD-9-CM Codes: 447.3, 447.8
- ICD-10-AM Codes: I77.3
Fibromuscular dysplasia (FMD) is a rare disease of medium to small arteries that has similar effects to atherosclerosis. It most commonly affects the renal and internal carotid arteries.
Confirming the diagnosis
The clinical presentation varies significantly with the arteries involved and the severity. In patients suspected of having this condition confirmation requires radiological imaging of involved arteries in the form of computed tomography angiography (CTA), magnetic resonance angiography (MRA), duplex ultrasonography, or digital substraction angiography (DSA), showing characteristic changes of FMD.
The relevant medical specialist is a physician.
Additional diagnoses covered by the SOP
Conditions not covered by the SOP
- atherosclerotic vascular disease
The first clinical evidence of FMD may be: hypertension that is severe, resistant to treatment, or of early onset; a cervical or abdominal bruit (an abnormal sound heard via a stethoscope over an affected artery); pulsatile tinnitus; evidence of ischaemic vascular disease or a variety of other manifestations. Advice on the timing of clinical onset should be sought from the treating physician if possible.
Appropriate treatment varies with the clinical presentation and may involve medical therapy or procedures/surgery to revascularise (reopen) occluded arteries. The condition will commonly progress despite optimal treatment. Specialist medical advice will generaly be required to establish whether there has been clinical worsening beyond the normal course of the disease.