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Creutzfeldt-Jakob Disease F005

Last amended 
Monday, February 15, 2021
Current RMA Instruments
Reasonable Hypothesis SOP [1]
76 of 2014
Balance of Probabilities SOP [2]
77 of 2014
Changes from previous Instruments

SOP Bulletin 177 [3]

ICD Coding
  • ICD-9-CM Codes: 046.1
  • ICD-10-AM Codes: A81.0
Brief description

This SOP covers both Creutzfeldt-Jakob disease (CJD), a rapidly progressive degenerative brain disorder, and variant CJD associated with mad cow disease.  CJD is a very rare disease.  No case of variant CJD has ever been reported in Australia (at Feb ‘21).

Confirming the diagnosis

This diagnosis is complex and requires diagnosis by a specialist neurologist or infectious disease physician, or confirmation by autopsy.

Additional diagnoses covered by SOP
  • Classical Creutzfeldt Jakob disease
  • Variant Creutzfeldt Jakob disease
Conditions excluded from SOP
  • Kuru - non SOP
  • Other forms of dementia
Clinical onset

Mean age of onset is around 60.  The typical clinical presentation is with rapid neuropsychiatric decline.

Clinical worsening

There are no clinical worsening factors in the SOP.

Rulebase for Creutzfeldt-Jakob disease

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Place holder node for Rulebase for Creutzfeldt-Jakob disease

Dura mater graft

Creutzfeldt-Jakob disease - Dura mater graft Factor

Last reviewed for CCPS 15 May 1998.

Preliminary questions [16286]

16375 [5] there is some evidence that undergoing a dura mater graft may be a factor in the development of the condition under consideration.

16313 [5] the veteran has undergone a dura mater graft at some time.

[6]16314

the veteran has undergone a dura mater graft before the clinical onset of Creutzfeldt-Jakob disease.

16316 — the veteran has established the causal connection between the dura mater graft and VEA service for Creutzfeldt-Jakob disease.

16317 — the veteran has established the causal connection between the identified illness or injury for which the dura mater graft was given and operational service for the clinical onset of Creutzfeldt-Jakob disease.

or

16318 — the veteran has established the causal connection between the identified illness or injury for which the dura mater graft was given and eligible service for the clinical onset of Creutzfeldt-Jakob disease.

Clinical onset and operational service [16317]

[7]24916

the veteran underwent a dura mater graft before the clinical onset of Creutzfeldt-Jakob disease on operational service. [8]

or

16315 — the dura mater graft was given for an illness or injury which is identifiable. [9]

16319 — the identified illness or injury for which the dura mater graft is causally related to operational service. [10] [11]

Clinical onset and eligible service [16318]

16315 — the dura mater graft was given for an illness or injury which is identifiable. [9]

16320 — the identified illness or injury for which the dura mater graft is causally related to eligible service. [12] [11]

Surgery to the central nervous system or cornea

Creutzfeldt-Jakob disease - Surgery to the central nervous system or cornea Factor

Last reviewed for CCPS 15 May 1998.

Preliminary questions [16285]

16305 [13] the veteran has had surgery to the central nervous system or cornea at some time.

[14]16306

the veteran had surgery to the central nervous system or cornea before the clinical onset of Creutzfeldt-Jakob disease.

16308 — the veteran has established the causal connection between the surgery to the central nervous system or cornea and VEA service for Creutzfeldt-Jakob disease.

16309 — the veteran has established the causal connection between the surgery to the central nervous system or cornea and operational service for the clinical onset of Creutzfeldt-Jakob disease.

or

16310 — the veteran has established the causal connection between the surgery to the central nervous system or cornea and eligible service for the clinical onset of Creutzfeldt-Jakob disease.

Clinical onset and operational service [16309]

[15]24915

the veteran had surgery to the central nervous system or cornea before the clinical onset of Creutzfeldt-Jakob disease on operational service.

or

[16]16307

the surgery to the central nervous system or cornea before the clinical onset of Creutzfeldt-Jakob disease was for an illness or injury which is identifiable.

16311 — the identified illness or injury for which the surgery to the central nervous system or cornea was given is causally related to operational service. [17] [18]

Clinical onset and eligible service [16310]

[19]16307

the surgery to the central nervous system or cornea before the clinical onset of Creutzfeldt-Jakob disease was for an illness or injury which is identifiable. [17]

16312 — the identified illness or injury for which the surgery to the central nervous system or cornea was given is causally related to eligible service. [20] [18]

Treatment with human pituitary gonadotrophins

Creutzfeldt-Jakob disease - Treatment with human pituitary gonadotrophins Factor

Last reviewed for CCPS 15 May 1998.

Preliminary questions [16284]

16374 [21] there is some evidence that treatment with human pituitary gonadotrophins may be a factor in the development of the condition under consideration.

1169 — the veteran is a woman. [22]

[21]16297

the veteran has had treatment with human pituitary gonadotrophins at some time.

[23]16298

the veteran had treatment with human pituitary gonadotrophins before the clinical onset of Creutzfeldt-Jakob disease.

16300 — the veteran has established the causal connection between the treatment with human pituitary gonadotrophins and VEA service for Creutzfeldt-Jakob disease.

16301 — the veteran has established the causal connection between the treatment with human pituitary gonadotrophins and operational service for the clinical onset of Creutzfeldt-Jakob disease.

or

16302 — the veteran has established the causal connection between the treatment with human pituitary gonadotrophins and eligible service for the clinical onset of Creutzfeldt-Jakob disease.

Clinical onset and operational service [16301]

[24]24914

the veteran had treatment with human pituitary gonadotrophins before the clinical onset of Creutzfeldt-Jakob disease on operational service.

or

[25]16299

the treatment with human pituitary gonadotrophins before the clinical onset of Creutzfeldt-Jakob disease was for an illness or injury which is identifiable.

16303 — the identified illness or injury for which treatment with human pituitary gonadotrophins was given is causally related to operational service. [26] [27]

Clinical onset and eligible service [16302]

[28]16299

the treatment with human pituitary gonadotrophins before the clinical onset of Creutzfeldt-Jakob disease was for an illness or injury which is identifiable. [26]

16304 — the identified illness or injury for which treatment with human pituitary gonadotrophins was given is causally related to eligible service. [29] [27]

Treatment with human pituitary growth hormone

Creutzfeldt-Jakob disease - Treatment with human pituitary growth hormone Factor

Last reviewed for CCPS 15 May 1998.

Preliminary questions [16283]

16373 [30] there is some evidence that treatment with human pituitary growth hormone may be a factor in the development of the condition under consideration.

16287 [30] the veteran has had treatment with human pituitary growth hormone at some time.

[31]16288

the veteran had treatment with human pituitary growth hormone before the clinical onset of Creutzfeldt-Jakob disease.

16289 — the veteran has established the causal connection between the treatment with human pituitary growth hormone and VEA service for Creutzfeldt-Jakob disease.

16292 — the veteran has established the causal connection between the treatment with human pituitary growth hormone and operational service for the clinical onset of Creutzfeldt-Jakob disease.

or

16293 — the veteran has established the causal connection between the treatment with human pituitary growth hormone and eligible service for the clinical onset of Creutzfeldt-Jakob disease.

Clinical onset and operational service [16292]

[32]24913

the veteran had treatment with human pituitary growth hormone before the clinical onset of Creutzfeldt-Jakob disease, on operational service.

or

[33]16294

the treatment with human pituitary growth hormone before the clinical onset of Creutzfeldt-Jakob disease was for an illness or injury which is identifiable.

16295 — the identified illness or injury for which treatment with human pituitary growth hormone was given is causally related to operational service. [34] [35]

Clinical onset and eligible service [16293]

[36]16294

the treatment with human pituitary growth hormone before the clinical onset of Creutzfeldt-Jakob disease was for an illness or injury which is identifiable. [34]

16296 — the identified illness or injury for which treatment with human pituitary growth hormone was given is causally related to eligible service. [37] [35]


Source URL (modified on 04/05/2021 - 8:49am): https://clik.dva.gov.au/ccps-medical-research-library/sops-grouped-icd-body-system/c-d/creutzfeldt-jakob-disease-f005-a810

Links
[1] http://www.rma.gov.au/assets/SOP/2014/076.pdf
[2] http://www.rma.gov.au/assets/SOP/2014/077.pdf
[3] https://clik.dva.gov.au/system/files/media/Bull177_5.pdf
[4] https://clik.dva.gov.au/user/login?destination=comment/reply/63446%23comment-form
[5] https://clik.dva.gov.au/ccpsf005rc-1
[6] clikpopup://CCPS/reject16313No
[7] clikpopup://CCPS/reject16314No
[8] clikpopup://CCPS/reject24916No
[9] clikpopup://CCPS/reject16315No
[10] clikpopup://CCPS/reject16319No
[11] clikpopup://CCPS/reject16319,16320No
[12] clikpopup://CCPS/reject16320No
[13] clikpopup://CCPS/Surgery to central nervous system or cornea at some time
[14] clikpopup://CCPS/reject16305No
[15] clikpopup://CCPS/reject16306No
[16] clikpopup://CCPS/reject24915No
[17] clikpopup://CCPS/reject16307No
[18] clikpopup://CCPS/reject16311,16312No
[19] clikpopup://CCPS/Surgery to central nervous system or cornea before CJD onset for illness
[20] clikpopup://CCPS/reject16312No
[21] https://clik.dva.gov.au/ccpsf005rc-11
[22] clikpopup://CCPS/reject1169No
[23] clikpopup://CCPS/reject16297No
[24] clikpopup://CCPS/reject16298No
[25] clikpopup://CCPS/reject24914No
[26] clikpopup://CCPS/reject16299No
[27] clikpopup://CCPS/reject16303,16304No
[28] clikpopup://CCPS/Treatment with human gonadotrophins before CJD onset for illness
[29] clikpopup://CCPS/reject16304No
[30] https://clik.dva.gov.au/ccpsf005rc-6
[31] clikpopup://CCPS/reject16287No
[32] clikpopup://CCPS/reject16288No
[33] clikpopup://CCPS/reject24913No
[34] clikpopup://CCPS/reject16294No
[35] clikpopup://CCPS/reject16295,16296No
[36] clikpopup://CCPS/Treatment with human growth hormone before CJD onset for illness
[37] clikpopup://CCPS/reject16296No